Division of Respirology

Adult Cystic Fibrosis

McMaster University Medical Centre
During this ambulatory rotation, the resident will see patients with cystic fibrosis (including adults) in a multidisciplinary regional clinic. You will develop an understanding of issues regarding both the pulmonary and extrapulmonary manifestations of cystic fibrosis. Activities such as genetic counselling and selection of patients for lung transplantation will be available. Sub-specialty clinics, such as immunology or pediatric asthma may be combined with this experience.

Medical Expert

  1. Demonstrate knowledge of epidemiology, genetics and natural history of cystic fibrosis.
  2. Understand how the diagnosis of cystic fibrosis is established, including the roles and limitations of the testing modalities available.
  3. Understand the pathophysiology of lung disease in cystic fibrosis.
  4. Understand the principles of microbiology as they apply to lung disease in cystic fibrosis, including the use of inhaled antibiotics and synergy testing.
  5. Understand in detail the therapy of CF pulmonary disease and its relationship to disease stage, including the timing of referral for transplantation.
  6. Manage pulmonary complications of cystic fibrosis, including infectious exacerbations, hemoptysis, and pneumothorax.
  7. Understand the diagnosis and management of pancreatic insufficiency and other gastrointestinal complications of cystic fibrosis.
  8. Understand the importance of nutrition in cystic fibrosis, the role and availability of various nutritional interventions.
  9. Gain experience in the management of cystic fibrosis-related diabetes mellitus.
  10. Gain experience in addressing issues of infertility and pregnancy in cystic fibrosis.
  11. Understand the factors that determine prognosis in cystic fibrosis.
  12. To be aware of new and experimental therapies being used in cystic fibrosis.

Communicator

  1. To develop rapport, trust and ethical therapeutic relationships with patients and families
  2. nsure that the cystic fibrosis patient to feels comfortable in the transfer of care between the pediatric to the adult cystic fibrosis team

Collaborator

To understand the role of members of the multidisciplinary cystic fibrosis team and how they work together for optimal patient care.

Manager

To recognize that a career Cystic Fibrosis physician must assume a leadership, managerial, administrative role along with participation in health care organizations.

Health Advocate

To recognize the need for transfer of care or mobilization of resources to serve the needs of cystic fibrosis patients living in non-academic centers who require tertiary level care.

Scholar

Articipate in the teaching of cystic fibrosis patients and their families about the various components of the disease with a focus on prevention of complications.

Professional

To be aware of the importance of patient confidentiality in young adult cystic fibrosis patients, who have recently come to an age where privacy and confidentiality must be respected.